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Phase 3 N=32 Randomized Quadruple-blind Treatment

Recombinant Human C1 Inhibitor for the Treatment of Acute Attacks in Patients With Hereditary Angioedema

Hereditary Angioedema · Angioneurotic Edema · Genetic Disorders

Enrolled (actual)
32
Serious AEs
2.3%
Results posted
Aug 2012
Primary outcome: Primary: Time to Beginning of Relief of Symptoms — 62; 508; 61 minutes — p=0.003

Study Design & Population

Study type
Interventional
Phase
Phase 3
Interventions
recombinant human C1 inhibitor (Drug); Placebo (Drug)
Age
Pediatric, Adult, Older Adult · 16+ yrs
Sex
All
Sponsor
Pharming Technologies B.V.
Primary completion
Jul 2009

Outcome Measures

OutcomeResultp-value
PRIMARY
Time to Beginning of Relief of Symptoms
62; 508; 61 0.003 sig
SECONDARY
Time to Minimal Symptoms
480; 1440; 241 0.005 sig

Summary

Hereditary angioedema ("HAE") is a genetic disorder characterized by sudden recurrent attacks of local swelling (angioedema). These attacks are often painful and disabling, and, in some cases, life-threatening. "HAE" is caused by mutations in the "C1INH" gene that leads to a decrease in the blood level of functional "C1INH". This multi-center study was designed to assess the safety and tolerability, efficacy and pharmacodynamics/ pharmacokinetics of recombinant human C1 inhibitor ("rhC1INH") in the treatment of acute hereditary angioedema attacks.

Eligibility Criteria

Inclusion Criteria

  • Clear clinical and laboratory diagnosis of HAE
  • Baseline plasma level of functional C1INH of less than 50% of normal
  • Evidence for exacerbation or development of a severe abdominal, oro-facial/ pharyngeal/ laryngeal, genito-urinary and/or peripheral HAE attack

Exclusion Criteria

  • Acquired angioedema
  • Pregnancy or breastfeeding
  • Participation in another clinical study within prior 3 months
View full record on ClinicalTrials.gov →

Data sourced from ClinicalTrials.gov (NCT00262301). Outcome figures and adverse-event rates are extracted automatically from the registry's posted results and are provided for clinician reference, not as a substitute for the primary publication.

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