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N/A N=267 Randomized Treatment

Early Intervention in Cystic Fibrosis Exacerbation

Cystic Fibrosis

Enrolled (actual)
267
Serious AEs
2.6%
Results posted
Oct 2017
Primary outcome: Primary: Change in FEV1 — -0.07; -0.08 Liters

Study Design & Population

Study type
Interventional
Phase
N/A
Interventions
Home lung function and symptom monitoring (Device)
Age
Pediatric, Adult, Older Adult · 14+ yrs
Sex
All
Sponsor
Johns Hopkins University
Primary completion
Aug 2015

Outcome Measures

OutcomeResultp-value
PRIMARY
Change in FEV1
-0.07; -0.08
SECONDARY
Cystic Fibrosis Respiratory Symptom Diary (CFRSD)
4.56; 0.45
SECONDARY
Pulmonary Exacerbations
70; 75
SECONDARY
Change in Health Related Quality of Life Scores as Assessed by the Cystic Fibrosis Questionnaire Revised (CFQ-R) (Respiratory Subscale Only(
-3.07; -.44
SECONDARY
Treatment Burden
0.6; 2.9
SECONDARY
Change in Prevalence of Resistant Species of Bacteria
3; 8
SECONDARY
Serious Adverse Events (SAE)
0.023; 0.030

Summary

Individuals with cystic fibrosis (CF) develop chronic lung infections and suffer intermittent acute exacerbations of their lung disease. Most exacerbations are not treated until they cause increased symptoms, and patients seek medical attention. This proposal details a study of home lung function and symptom monitoring. Subjects will be randomly assigned to one of two groups: 1) home monitoring, in which spirometry and symptoms are recorded; or 2) standard care. The home monitoring data will be transmitted electronically to the study center. If spirometry or symptoms have deteriorated substantially, treatment for a CF pulmonary exacerbation will be initiated. It is anticipated that use of home monitoring will lead to earlier, more reliable recognition and treatment of exacerbations, which will translate into better lung health.

Eligibility Criteria

Inclusion Criteria

  • CF diagnosis confirmed with sweat test, abnormal nasal potential difference and/or genetic testing
  • Age 14 and older
  • Able to perform spirometry
  • Clinically stable without antibiotic treatment for a pulmonary exacerbation in the two weeks prior to the screening visit
  • Forced expiratory volume in the first second (FEV1) greater than 25% of predicted at screening

Exclusion Criteria

  • History of solid organ transplant
  • Participation in any interventional trial within the last 30 days
  • Inability to speak and read the English language well enough to complete questionnaires
  • Colonization with Burkholderia cepacia genomovar III within the last 24 months
  • Currently receiving antimicrobial treatment specifically used to treat active non-tuberculosis mycobacterium
  • Confirmed diagnosis of allergic bronchopulmonary aspergillosis (ABPA) as defined by the Cystic Fibrosis Foundation (CFF) guidance document that is being actively treated
View full record on ClinicalTrials.gov →

Data sourced from ClinicalTrials.gov (NCT01104402). Outcome figures and adverse-event rates are extracted automatically from the registry's posted results and are provided for clinician reference, not as a substitute for the primary publication.

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