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Phase 2 N=6 Basic Science

A Proof-of-Mechanism Study to Determine the Effect of Danicopan on C3 Levels in Participants With C3G or IC-MPGN

C3 Glomerulonephritis · Dense Deposit Disease · C3 Glomerulopathy · Immune Complex Mediated Membranoproliferative Glomerulonephritis · Membranoproliferative Glomerulonephritis Types I, II, and III

Enrolled (actual)
6
Serious AEs
16.7%
Results posted
Jul 2021
Primary outcome: Primary: Change From Baseline In Serum C3 Complement Protein (C3) Levels On Day 15 — 0.32; 0.56; 0.48; 0.35 g/L

Study Design & Population

Study type
Interventional
Phase
Phase 2
Interventions
Danicopan (Drug)
Age
Pediatric, Adult, Older Adult · 16+ yrs
Sex
All
Sponsor
Alexion Pharmaceuticals, Inc.
Primary completion
Dec 2018

Outcome Measures

OutcomeResultp-value
PRIMARY
Change From Baseline In Serum C3 Complement Protein (C3) Levels On Day 15
0.32; 0.56; 0.48; 0.35; 0.70; 0.58
PRIMARY
Change From Baseline In Plasma Intact C3 Level On Day 15
39.50; 58.25; 52.00; 54.30; 33.50; 40.43
SECONDARY
Change From Baseline In Total Complement Classical Pathway (CP) Activity On Day 14
31.00; 91.00; 71.00; 41.50; 96.75; 78.33
SECONDARY
Change From Baseline In Total Complement Alternative Pathway (AP) Functional Activity (AP Wieslab) On Day 15
8.350; 31.073; 23.498; 1.635; 0.993; 1.207
SECONDARY
Time To Achieving Peak Serum C3 Levels
2.5; 10.5; 7.8
SECONDARY
Number Of Participants With Serious Adverse Events (SAEs), Grade 3 And Grade 4 Treatment-emergent Adverse Events (TEAEs), And Adverse Events (AEs) Leading To Discontinuation
2; 3; 5; 0; 1; 1
SECONDARY
Pharmacokinetics (PK): Area Under The Plasma Concentration-time Curve From Time Of Administration To 8 Hours Postdose (AUC0-8)
871; 2060; 1640; 1120; 2470; 1760
SECONDARY
PK: Maximum Plasma Concentration (Cmax)
199; 563; 427; 270; 579; 385
SECONDARY
PK: Time To Maximum Concentration (Tmax)
1.00; 2.50; 2.00; 2.75; 2.50; 1.50
SECONDARY
Change From Baseline In Bb Fragment Of Complement Factor B (Bb) At Day 15
1.789; 1.229; 1.416; 1.511; 0.622; 0.918
SECONDARY
Change From Baseline In Soluble Terminal Complement Complex (sC5b-9) At Day 15
1002.0; 613.750; 743.167; 1105.5; 563.850; 744.400

Summary

The primary objective of this study was to determine whether ACH-0144471 (also known as danicopan and ALXN2040) increases blood C3 complement protein (C3) levels in participants with low C3 levels due to either C3G or IC-MPGN.

Eligibility Criteria

Key Inclusion Criteria

  • Must have had clinical diagnosis of C3G (C3 glomerulonephritis or dense deposit disease, the 2 types of C3G) or idiopathic IC-MPGN by renal biopsy for at least 3 months prior to dosing, with the pathologic diagnosis verified by a review of the renal biopsy by the study central pathologist
  • C3 must have been 90% of the lower limit of normal
  • Must have been willing to comply with study-specific vaccination requirements for Haemophilus influenzae, Streptococcus pneumoniae, and Neisseria meningitidis strains A, C, W, and Y
  • Negative pregnancy test for females prior to dosing and throughout the study

Key Exclusion Criteria

  • History of a major organ transplant (for example, heart, lung, kidney, liver) or hematopoietic stem cell/marrow transplant. Individuals receiving renal replacement therapy were also excluded
  • Evidence of monoclonal gammopathy of unclear significance, infections, malignancy, autoimmune diseases, or other conditions to which C3G or IC-MPGN may have been secondary
  • Estimated glomerular filtration rate (using Modification of Diet in Renal Disease equation) 38°Celsius, or other evidence of a clinically significant active infection, within 14 days prior to study drug administration
  • History of meningococcal infection, or a first-degree relative or household contact with a history of meningococcal infection
  • Females who were pregnant, nursing, or planning to become pregnant during the study or within 90 days of study drug administration or participants with a female partner who was pregnant, nursing, or planning to become pregnant during the study or within 90 days of study drug administration
View full record on ClinicalTrials.gov →

Data sourced from ClinicalTrials.gov (NCT03124368). Outcome figures and adverse-event rates are extracted automatically from the registry's posted results and are provided for clinician reference, not as a substitute for the primary publication.

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