Mode
Text Size
Log in / Sign up
Phase 3 Completed N=387 Prevention

A Long Term Safety Study of BCX7353 in Hereditary Angioedema

Hereditary Angioedema · HAE · Prophylaxis
Source: ClinicalTrials.gov NCT03472040 ↗
Enrolled (actual)
387
Serious AEs
11.1%
Results posted
Jun 2023
Primary outcomePrimary: Safety & Tolerability — 94; 240; 58; 119 Participants
◆ Published Evidence
Emerging
13citations · ~3 / year
Shared decision-making in the management of hereditary angioedema: An analysis of patient and physician perspectives.
Allergy and asthma proceedings · 2022 · Likely link

Summary

This is an open-label study to evaluate the long term safety and effectiveness of oral treatment with BCX7353 in preventing acute angioedema attacks in patients with Type I and Type II Hereditary Angioedema (HAE).

Linked Publications (5)

  • Shared decision-making in the management of hereditary angioedema: An analysis of patient and physician perspectives.
    Allergy and asthma proceedings · 2022 · 13 citations · Likely link
  • Hereditary angioedema outcomes in US patients switched from injectable long-term prophylactic medication to oral berotralstat.
    Annals of allergy, asthma & immunology : official publication of the American College of Allergy, Asthma, & Immunology · 2024 · 10 citations · Likely link
  • Assessment of HAE prophylaxis transition from androgen therapy to berotralstat: A subset analysis of the APeX-S trial.
    The World Allergy Organization journal · 2023 · 8 citations · Open access · Likely link
  • A review of berotralstat for the treatment of hereditary angioedema.
    Expert review of clinical immunology · 2023 · 7 citations · Likely link
  • Long-term safety and efficacy of once-daily berotralstat in patients with hereditary angioedema: APeX-S final results.
    Annals of allergy, asthma & immunology : official publication of the American College of Allergy, Asthma, & Immunology · 2025 · 6 citations · Open access · Likely link

Outcome Measures

OutcomeResultp-value
PRIMARY
Safety & Tolerability
94; 240; 58; 119; 23; 20
SECONDARY
Incidence of Acute Attacks of Angioedema in Subjects During Treatment
95; 231; 87; 214; 59; 99
SECONDARY
The Durability of Response to Treatment
1.276; 1.079; 1.005; 0.694; 1.121; 0.591
SECONDARY
Patient Reported Quality of Life (QoL) During Treatment
-8.85; -10.38; -11.20; -10.39; -11.92; -11.47
SECONDARY
Patient's Satisfaction With Medication During Long Term Administration of Berotralstat
-4.1; -1.3; -0.6; -3.6; 1.5; -0.1

Eligibility Criteria

Key Inclusion Criteria

  • Subjects with HAE Type I or II who either have participated in a previous BCX7353 study or, in selected countries, in the opinion of the Investigator are expected to derive benefit from an oral treatment for the prevention of angioedema attacks.
  • Access to appropriate medication for treatment of acute attacks
  • Acceptable effective contraception
  • Written informed consent

Key Exclusion Criteria

  • Pregnancy or breast-feeding
  • Any clinically significant medical condition or medical history that, in the opinion of the Investigator or Sponsor, would interfere with the subject's safety or ability to participate in the study
  • Any laboratory parameter abnormality that, in the opinion of the Investigator, is clinically significant and relevant for this study
  • Discontinuation of study drug due to a hypersensitivity reaction BCX7353 in a prior study
  • Severe hypersensitivity to multiple medicinal products or severe hypersensitivity/ anaphylaxis with unclear etiology
  • Unacceptable noncompliance in a previous BCX7353 study (if applicable) as assessed by the Sponsor or Investigator
  • Investigational drug exposure, other than BCX7353, within 30 days prior to the screening visit (or baseline if no screening visit)
View full record on ClinicalTrials.gov →

Data sourced from ClinicalTrials.gov (NCT03472040) and the linked publication. Outcome figures and adverse-event rates are extracted automatically from the registry's posted results and are provided for clinician reference, not as a substitute for the primary publication. Informational only — not medical advice.

Back to search