Retrospective review of methylprednisolone response in children with TBX4-associated pulmonary hypertension and interstitial lung disease.
Pulsed steroids may help children with TBX4-linked lung disease and pulmonary hypertension
This review examines a retrospective cohort of 21 children with TBX4-associated pulmonary hypertension treated with methylprednisolone. Auth…
Pulsed steroids helped most children with TBX4-linked lung disease improve breathing and heart function without significant side effects.